The pathologic findings highlight the importance of thorough sampling for histology in polycystic kidney diseases and indicate that the observation of an angiomyolipoma in biopsy material from patients with enlarged cystic kidneys should suggest the diagnosis of TSC2/PKD1 contiguous gene syndrome, even in cases without ultrasonographic and macroscopic evidence of angiomyolipoma..     ///    Renal disease in adults with TSC2/PKD1 contiguous gene syndrome..     ///    This disease has been termed the TSC2/PKD1 contiguous gene syndrome. 